Solitary Langerhans Cell Histiocytosis of Skull: Case Report with One-year Follow-up

نویسندگان

چکیده

Langerhans cell histiocytosis (LCH) is a rare disorder characterised by increased production of Langerhans-type histiocytes. It more common in the pediatric age group with predilection for osseous involvement, though any organ may be involved. A 10-year male child was brought to neurosurgical clinic slow growing painful tender mass on head. Initial attempt biopsy lesion failed due excessive bleeding. later imaged and removed frontal craniotomy. Histopathological evaluation along immunohistochemistry revealed true nature lesion. Follow-up complete excision no recurrence at one-year after surgery. Key Words: histiocytosis, Pediatric age, Skull.

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ژورنال

عنوان ژورنال: JCPSP. Journal of the College of Physicians & Surgeons Pakistan

سال: 2021

ISSN: ['1022-386X', '1681-7168']

DOI: https://doi.org/10.29271/jcpsp.2021.08.989